vitalwiki

Behavioral variant of frontotemporal dementia

ORPHA:275864· ICD-10 G31.0

Definition

Behavioral variant of frontotemporal dementia (bv-FTD) is a form of frontotemporal dementia (FTD), characterized by progressive behavioral impairment and a decline in executive function with frontal lobe-predominant atrophy.

Prevalence
1-9 / 100 000
Inheritance
Autosomal dominant
Age of onset
Adult