Pulmonary arterial hypertension associated with chronic hemolytic anemia
ORPHA:275828
Definition
Pulmonary arterial hypertension associated with chronic hemolytic anemia (PAH-CHA) is a form of PAH characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of chronic hemolytic anemia.
- Prevalence
- Unknown
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- All ages