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Odontomatosis-aortae esophagus stenosis syndrome

ORPHA:2724· ICD-10 D16.5

Definition

Odontoma-dysphagia syndrome is a malformation syndrome, characterized by odontomas (undifferentiated mass of the esophagus) and severe dysphagia.

Prevalence
<1 / 1 000 000
Age of onset
No data available