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Fuchs heterochromic iridocyclitis

ORPHA:263479· ICD-10 H20.8

Definition

Fuchs heterochromic iridocyclitis (FHI) is an ocular disease of unknown etiology occurring in a very small percentage (0.5-6.2%) of uvietis cases, characterized by diffuse iris heterochromia or atrophy, keratic precipitates in the absence of synechiae, and in some cases evolving to glaucoma and vitreous opacities.

Prevalence
1-9 / 1 000 000
Age of onset
Adult