Congenital pulmonary lymphangiectasia
ORPHA:2414· ICD-10 Q33.8
Definition
A rare developmental disorder involving the lung and characterized by pulmonary subpleural, interlobar, perivascular, and peribronchial lymphatic dilatation.
- Prevalence
- Unknown
- Inheritance
- Autosomal recessive
- Age of onset
- Neonatal