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Muscular pseudohypertrophy-hypothyroidism syndrome

ORPHA:2349· ICD-10 E03.1

Definition

Muscular pseudohypertrophy - hypothyroidism, also known as Kocher-Debre-Semelaigne syndrome is a rare disorder characterized by pseudohypertrophy of muscles due to longstanding hypothyroidism.

Prevalence
Unknown
Age of onset
Childhood