Kasabach-Merritt phenomenon
ORPHA:2330· ICD-10 D18.0
Definition
A rare hemorrhagic disorder characterized by potentially life-threatening thrombocytopenia, microangiopathic hemolytic anemia, and consumptive coagulopathy in the context of kaposiform hemangioendothelioma or tufted angioma.
- Prevalence
- Unknown
- Inheritance
- Not applicable
- Age of onset
- Infancy, Neonatal