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Linear focal elastosis

ORPHA:228236· ICD-10 L98.8

Definition

Linear focal elastosis is a rare, acquired, dermis elastic tissue disorder characterized by asymptomatic, palpable, hypertrophic or atrophic, yellowish or red, indurated, horizontal, striae-like linear plaques distributed symmetrically across the mid and lower back. No systemic involvement has been described. Skin biopsy reveals a focal increase in abnormal elastic tissue with abundant, wavy, fragmented and aggregated, basophilic elastic fibers in the reticular dermis.

Prevalence
<1 / 1 000 000
Inheritance
Not applicable
Age of onset
All ages