Linear focal elastosis
ORPHA:228236· ICD-10 L98.8
Definition
Linear focal elastosis is a rare, acquired, dermis elastic tissue disorder characterized by asymptomatic, palpable, hypertrophic or atrophic, yellowish or red, indurated, horizontal, striae-like linear plaques distributed symmetrically across the mid and lower back. No systemic involvement has been described. Skin biopsy reveals a focal increase in abnormal elastic tissue with abundant, wavy, fragmented and aggregated, basophilic elastic fibers in the reticular dermis.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Not applicable
- Age of onset
- All ages