Hypoplastic left heart syndrome
ORPHA:2248· ICD-10 Q23.4
Definition
A rare, congenital, non-syndromic, heart malformation characterized by under development of the left-sided cardiac structures (including left ventricle, ascending aorta, aortic arch, and mitral and/or aortic valve) such that the left heart is unable to provide adequate systemic cardiac output.
- Prevalence
- 1-5 / 10 000
- Inheritance
- Unknown
- Age of onset
- Antenatal, Neonatal