Limited cutaneous systemic sclerosis
ORPHA:220402· ICD-10 M34.1
Definition
Limited cutaneous systemic sclerosis (lcSSc) is a subtype of systemic sclerosis (SSc) characterized by the association of Raynaud's phenomenon with skin fibrosis limited to the hands, face, feet and forearms.
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- Adult