Adenosarcoma of the cervix uteri
ORPHA:213792· ICD-10 C53.0
Definition
A rare subtype of malignant mixed epithelial and mesenchymal tumor composed of benign or mildly atypical glandular elements and a surrounding low-grade malignant stroma, often containing heterologous elements, such as areas of sex-cord-like or smooth muscle differentiation. It usually presents with vaginal bleeding or discharge, lower abdominal pain and/or a cervical mass or polyp. The tumor may arise from pre-existing endometriosis and patients may have a history of recurrent cervical polyps.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Adolescent, Adult, Elderly