Congenital respiratory-biliary fistula
ORPHA:2040· ICD-10 Q32.4
Definition
Congenital respiratory-biliary fistula (RBF) is a rare developmental defect characterized by an anomalous connection of trachea or bronchus with left hepatic duct presenting with respiratory distress, recurrent respiratory infections and biliary expectoration or vomitus.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Not applicable
- Age of onset
- Childhood