Pulmonary arteriovenous malformation
ORPHA:2038· ICD-10 Q25.7
Definition
An aberrant communication between one or more pulmonary arteries and one or more pulmonary veins leading to an anatomic intrapulmonary right-to-left shunt.
- Prevalence
- 1-9 / 100 000
- Inheritance
- Multigenic/multifactorial, Unknown
- Age of onset
- Infancy