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Eosinophilic granulomatosis with polyangiitis

ORPHA:183· ICD-10 M30.1

Definition

A rare systemic vasculitis of small vessels characterized by asthma, blood and tissue eosinophilia and vasculitis manifestations.

Prevalence
1-9 / 100 000
Inheritance
Not applicable
Age of onset
Adolescent, Adult, Elderly