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Mycosis fungoides and variants

ORPHA:178566· ICD-10 C84.0

Definition

A group of cutaneous T-cell lymphomas characterized by the indolent, slow progression of patches, plaques, and tumors. There are four known variants: classic mycosis fungoides, folliculotropic mycosis fungoides, localized pagetoid reticulosis and granulomatous slack skin. Classic MF is characterized by slow progression from patches on sun-protracted areas to more infiltrated plaques and tumors; folliculotropic MF preferentially involves the head and neck region; localized pagetoid reticulosis shows localized patches or plaques, usually involving one extremity; granulomatous slack skin is extremely rare and characterized by the presence of circumscribed areas of pendulous lax skin.

Prevalence
Unknown
Inheritance
Not applicable
Age of onset
Adult