Dentin dysplasia
ORPHA:1653· ICD-10 K00.5
Definition
Dentin dysplasia (DD) is a rare disorder belonging to the group of hereditary dentin defects and is characterized by abnormal dentin structure and root development resulting in abnormal tooth development. It encompasses two subtypes: DD type I and DD type II.
- Prevalence
- Unknown
- Inheritance
- Autosomal dominant
- Age of onset
- All ages