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Atrial septal defect-atrioventricular conduction defects syndrome

ORPHA:1479· ICD-10 Q21.1

Definition

An extremely rare genetic congenital heart disease characterized by the presence of atrial septal defect, mostly of the ostium secundum type, associated with conduction anomalies like atrioventricular block, atrial fibrillation or right bundle branch block.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
No data available