Carney triad
ORPHA:139411· ICD-10 D44.8
Definition
A rare non-hereditary condition characterized by gastrointestinal stromal tumors (GIST, intramural mesenchymal tumors of the gastrointestinal tract with neuronal or neural crest cell origin), pulmonary chondromas and extraadrenal paragangliomas.
- Prevalence
- <1 / 1 000 000
- Age of onset
- Adolescent, Adult