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Madras motor neuron disease

ORPHA:137867· ICD-10 G12.2

Definition

Madras motor neuron disease (MMND) is characterized by weakness and atrophy of limbs, multiple lower cranial nerve palsies and sensorineural hearing loss.

Prevalence
<1 / 1 000 000
Inheritance
Not applicable, X-linked recessive
Age of onset
Adolescent, Adult, Childhood