Histiocytoid cardiomyopathy
ORPHA:137675· ICD-10 I42.0
Definition
A rare arrhythmogenic disorder characterized by cardiomegaly, severe cardiac arrhythmias or sudden death, and the presence of histiocyte-like cells within the myocardium.
- Prevalence
- <1 / 1 000 000
- Inheritance
- Autosomal recessive, Unknown, X-linked dominant
- Age of onset
- Infancy, Neonatal