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Isolated atrial standstill

ORPHA:1344· ICD-10 I45.5

Definition

A rare cardiac rhythm disease characterized by a transient or permanent absence of electrical and mechanical atrial activity. Electrocardiographic findings include bradycardia, ectopic supraventricular rhythms, lack of atrial excitability and absent P waves.

Prevalence
Unknown
Inheritance
Autosomal dominant, Not applicable
Age of onset
Adult