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Bazex-Dupré-Christol syndrome

ORPHA:113· ICD-10 L98.8

Definition

Bazex-Dupré-Christol syndrome is a rare genodermatosis with a predisposition to early-onset basal cell carcinomas.

Prevalence
<1 / 1 000 000
Inheritance
X-linked dominant
Age of onset
Infancy, Neonatal