vitalwiki

Leber hereditary optic neuropathy

ORPHA:104· ICD-10 H47.2

Definition

A rare hereditary optic neuropathy characterized by sudden onset, painless central vision loss, loss of retinal ganglion cells and optic atrophy.

Prevalence
1-9 / 100 000
Inheritance
Mitochondrial inheritance
Age of onset
Adolescent, Adult