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Chronic primary adrenal insufficiency

ORPHA:101959

Definition

Chronic primary adrenal insufficiency (CPAI) is a chronic disorder of the adrenal cortex resulting in the inadequate production of glucocorticoid and mineralocorticoid hormones.

Prevalence
1-9 / 1 000 000
Inheritance
Multigenic/multifactorial
Age of onset
All ages