Middle ear neuroendocrine tumor
ORPHA:100084· ICD-10 C30.1
Definition
Middle ear neuroendocrine tumor is a rare, otorhinolaryngologic tumor characterized by a mixed glandular and non-glandular histological features and positive immunostaining for pancytokeratin, vimentin, synaptophysin and islet-1 protein. Common signs and symptoms are hearing loss, mass, pain, discharge, equilibrium disturbances, tinnitus and nerve paralysis.
- Age of onset
- Adolescent, Adult, Elderly