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Hereditary angioedema type 2

ORPHA:100051· ICD-10 D84.1

Definition

Hereditary angioedema type 2 (HAE 2) is a form of hereditary angioedema characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway.

Prevalence
Unknown
Inheritance
Autosomal dominant
Age of onset
All ages