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ABeta amyloidosis, Dutch type

ORPHA:100006· ICD-10 E85.4+

Definition

A form of hereditary cerebral hemorrhage with amyloidosis characterized by severe cerebral amyloid angiopathy (CAA), predominantly hemorrhagic strokes and dementia.

Prevalence
<1 / 1 000 000
Inheritance
Autosomal dominant
Age of onset
Adult